Mitoproteome Database (Select MITO_ID for details on gene/protein of interest)

MITO IDEntrez Gene IDGene nameSymbol
MT001037 51166 aminoadipate aminotransferase AADAT
MT001222 57505 alanyl-tRNA synthetase 2, mitochondrial AARS2
MT000755 10157 aminoadipate-semialdehyde synthase AASS
MT000001 18 4-aminobutyrate aminotransferase ABAT
MT000939 26154 ATP-binding cassette, sub-family A (ABC1), member 12 ABCA12
MT000771 10351 ATP-binding cassette, sub-family A (ABC1), member 8 ABCA8
MT000770 10350 ATP-binding cassette, sub-family A (ABC1), member 9 ABCA9
MT000889 23456 ATP-binding cassette, sub-family B (MDR/TAP), member 10 ABCB10
MT000745 10058 ATP-binding cassette, sub-family B (MDR/TAP), member 6
(Langereis blood group)		 ABCB6
MT000002 22 ATP-binding cassette, sub-family B (MDR/TAP), member 7 ABCB7
MT000843 11194 ATP-binding cassette, sub-family B (MDR/TAP), member 8 ABCB8
MT000025 215 ATP-binding cassette, sub-family D (ALD), member 1 ABCD1
MT000030 225 ATP-binding cassette, sub-family D (ALD), member 2 ABCD2
MT000522 5825 ATP-binding cassette, sub-family D (ALD), member 3 ABCD3
MT000538 6059 ATP-binding cassette, sub-family E (OABP), member 1 ABCE1
MT000747 10061 ATP-binding cassette, sub-family F (GCN20), member 2 ABCF2
MT000725 9619 ATP-binding cassette, sub-family G (WHITE), member 1 ABCG1
MT000707 9429 ATP-binding cassette, sub-family G (WHITE), member 2
(Junior blood group)		 ABCG2
MT001157 55347 abhydrolase domain containing 10 ABHD10
MT001375 83451 abhydrolase domain containing 11 ABHD11
MT001219 57406 abhydrolase domain containing 6 ABHD6
MT000003 25 ABL proto-oncogene 1, non-receptor tyrosine kinase ABL1
MT000778 10449 acetyl-CoA acyltransferase 2 ACAA2
MT000004 31 acetyl-CoA carboxylase α ACACA
MT000005 32 acetyl-CoA carboxylase β ACACB
MT001358 80724 acyl-CoA dehydrogenase family, member 10 ACAD10
MT001390 84129 acyl-CoA dehydrogenase family, member 11 ACAD11
MT000954 27034 acyl-CoA dehydrogenase family, member 8 ACAD8
MT000979 28976 acyl-CoA dehydrogenase family, member 9 ACAD9
MT000006 33 acyl-CoA dehydrogenase, long chain ACADL
MT000007 34 acyl-CoA dehydrogenase, C-4 to C-12 straight chain ACADM
MT000008 35 acyl-CoA dehydrogenase, C-2 to C-3 short chain ACADS
MT000009 36 acyl-CoA dehydrogenase, short/branched chain ACADSB
MT000010 37 acyl-CoA dehydrogenase, very long chain ACADVL
MT000011 38 acetyl-CoA acetyltransferase 1 ACAT1
MT001263 64746 acyl-CoA binding domain containing 3 ACBD3
MT000012 47 ATP citrate lyase ACLY
MT001205 57001 ACN9 homolog (S. cerevisiae) ACN9
MT000013 48 aconitase 1, soluble ACO1
MT000014 50 aconitase 2, mitochondrial ACO2
MT001183 55856 acyl-CoA thioesterase 13 ACOT13
MT000823 10965 acyl-CoA thioesterase 2 ACOT2
MT000852 11332 acyl-CoA thioesterase 7 ACOT7
MT000742 10005 acyl-CoA thioesterase 8 ACOT8
MT000900 23597 acyl-CoA thioesterase 9 ACOT9
MT000015 51 acyl-CoA oxidase 1, palmitoyl ACOX1
MT000652 8310 acyl-CoA oxidase 3, pristanoyl ACOX3
MT001039 51205 acid phosphatase 6, lysophosphatidic ACP6
MT001363 81616 acyl-CoA synthetase bubblegum family member 2 ACSBG2
MT001347 80221 acyl-CoA synthetase family member 2 ACSF2
MT001585 197322 acyl-CoA synthetase family member 3 ACSF3
MT000216 2180 acyl-CoA synthetase long-chain family member 1 ACSL1
MT000217 2181 acyl-CoA synthetase long-chain family member 3 ACSL3
MT000218 2182 acyl-CoA synthetase long-chain family member 4 ACSL4
MT001070 51703 acyl-CoA synthetase long-chain family member 5 ACSL5
MT000879 23305 acyl-CoA synthetase long-chain family member 6 ACSL6
MT001497 116285 acyl-CoA synthetase medium-chain family member 1 ACSM1
MT001513 123876 acyl-CoA synthetase medium-chain family member 2A ACSM2A
MT001644 348158 acyl-CoA synthetase medium-chain family member 2B ACSM2B
MT000546 6296 acyl-CoA synthetase medium-chain family member 3 ACSM3
MT001640 341392 acyl-CoA synthetase medium-chain family member 4 ACSM4
MT001114 54988 acyl-CoA synthetase medium-chain family member 5 ACSM5
MT001555 142827 acyl-CoA synthetase medium-chain family member 6 ACSM6
MT001411 84532 acyl-CoA synthetase short-chain family member 1 ACSS1
MT001314 79611 acyl-CoA synthetase short-chain family member 3 ACSS3
MT000016 98 acylphosphatase 2, muscle type ACYP2
MT000646 8038 ADAM metallopeptidase domain 12 ADAM12
MT001179 55803 ArfGAP with dual PH domains 2 ADAP2
MT001213 57143 aarF domain containing kinase 1 ADCK1
MT001456 90956 aarF domain containing kinase 2 ADCK2
MT001204 56997 aarF domain containing kinase 3 ADCK3
MT001335 79934 aarF domain containing kinase 4 ADCK4
MT001592 203054 aarF domain containing kinase 5 ADCK5
MT000017 128 alcohol dehydrogenase 5 (class III), chi polypeptide ADH5
MT001545 137872 alcohol dehydrogenase, iron containing, 1 ADHFE1
MT001431 84890 2-aminoethanethiol (cysteamine) dioxygenase ADO
MT001103 54936 ADP-ribosylhydrolase like 2 ADPRHL2
MT000961 27125 AF4/FMR2 family, member 4 AFF4
MT000819 10939 AFG3-like AAA ATPase 2 AFG3L2
MT001501 116986 ArfGAP with GTPase domain, ankyrin repeat and PH domain 2 AGAP2
MT001175 55750 acylglycerol kinase AGK
MT001329 79814 agmatine ureohydrolase (agmatinase) AGMAT
MT001154 55326 1-acylglycerol-3-phosphate O-acyltransferase 5 AGPAT5
MT000662 8540 alkylglycerone phosphate synthase AGPS
MT000791 10551 anterior gradient 2 AGR2
MT000877 23287 ATP/GTP binding protein 1 AGTPBP1
MT000018 189 alanine-glyoxylate aminotransferase AGXT
MT001271 64902 alanine--glyoxylate aminotransferase 2 AGXT2
MT000696 9131 apoptosis-inducing factor, mitochondrion-associated, 1 AIFM1
MT001430 84883 apoptosis-inducing factor, mitochondrion-associated, 2 AIFM2
MT001559 150209 apoptosis-inducing factor, mitochondrion-associated, 3 AIFM3
MT000693 9049 aryl hydrocarbon receptor interacting protein AIP
MT000019 204 adenylate kinase 2 AK2
MT001005 50808 adenylate kinase 3 AK3
MT000020 205 adenylate kinase 4 AK4
MT000648 8165 A kinase (PRKA) anchor protein 1 AKAP1
MT000846 11216 A kinase (PRKA) anchor protein 10 AKAP10
MT000766 10270 A kinase (PRKA) anchor protein 8 AKAP8
MT000021 207 v-akt murine thymoma viral oncogene homolog 1 AKT1
MT000741 10000 v-akt murine thymoma viral oncogene homolog 3 AKT3
MT000022 211 5'-aminolevulinate synthase 1 ALAS1
MT000023 212 5'-aminolevulinate synthase 2 ALAS2
MT000024 213 albumin ALB
MT000526 5832 aldehyde dehydrogenase 18 family, member A1 ALDH18A1
MT000027 219 aldehyde dehydrogenase 1 family, member B1 ALDH1B1
MT000808 10840 aldehyde dehydrogenase 1 family, member L1 ALDH1L1
MT001571 160428 aldehyde dehydrogenase 1 family, member L2 ALDH1L2
MT000026 217 aldehyde dehydrogenase 2 family (mitochondrial) ALDH2
MT000029 224 aldehyde dehydrogenase 3 family, member A2 ALDH3A2
MT000668 8659 aldehyde dehydrogenase 4 family, member A1 ALDH4A1
MT000640 7915 aldehyde dehydrogenase 5 family, member A1 ALDH5A1
MT000361 4329 aldehyde dehydrogenase 6 family, member A1 ALDH6A1
MT000050 501 aldehyde dehydrogenase 7 family, member A1 ALDH7A1
MT000028 223 aldehyde dehydrogenase 9 family, member A1 ALDH9A1
MT000031 230 aldolase C, fructose-bisphosphate ALDOC
MT000685 8846 alkB, alkylation repair homolog 1 (E. coli) ALKBH1
MT001599 221120 alkB, alkylation repair homolog 3 (E. coli) ALKBH3
MT001397 84266 alkB, alkylation repair homolog 7 (E. coli) ALKBH7
MT000032 239 arachidonate 12-lipoxygenase ALOX12
MT000901 23600 α-methylacyl-CoA racemase AMACR
MT001166 55626 autophagy/beclin-1 regulator 1 AMBRA1
MT000033 275 aminomethyltransferase AMT
MT000037 301 annexin A1 ANXA1
MT000844 11199 annexin A10 ANXA10
MT000121 1173 adaptor-related protein complex 2, mu 1 subunit AP2M1
MT000039 328 APEX nuclease (multifunctional DNA repair enzyme) 1 APEX1
MT000969 27301 APEX nuclease (apurinic/apyrimidinic endonuclease) 2 APEX2
MT001524 128240 apolipoprotein A-I binding protein APOA1BP
MT001307 79135 apolipoprotein O APOO
MT001548 139322 apolipoprotein O-like APOOL
MT001408 84334 apoptogenic 1, mitochondrial APOPT1
MT000040 369 A-Raf proto-oncogene, serine/threonine kinase ARAF
MT000041 384 arginase 2 ARG2
MT001131 55082 arginine and glutamate rich 1 ARGLU1
MT000042 402 ADP-ribosylation factor-like 2 ARL2
MT000896 23568 ADP-ribosylation factor-like 2 binding protein ARL2BP
MT000790 10550 ADP-ribosylation factor-like 6 interacting protein 5 ARL6IP5
MT001137 55156 armadillo repeat containing 1 ARMC1
MT001382 83787 armadillo repeat containing 10 ARMC10
MT001061 51566 armadillo repeat containing, X-linked 3 ARMCX3
MT001653 387715 age-related maculopathy susceptibility 2 ARMS2
MT000043 409 arrestin, β 2 ARRB2
MT000044 411 arylsulfatase B ARSB
MT001220 57412 arsenite methyltransferase AS3MT
MT001193 56624 N-acylsphingosine amidohydrolase (non-lysosomal ceramidase)
2		 ASAH2
MT001550 140462 ankyrin repeat and SOCS box containing 9 ASB9
MT000045 445 argininosuccinate synthase 1 ASS1
MT001432 84896 ATPase family, AAA domain containing 1 ATAD1
MT001145 55210 ATPase family, AAA domain containing 3A ATAD3A
MT001384 83858 ATPase family, AAA domain containing 3B ATAD3B
MT001441 85300 ataxia, cerebellar, Cayman type ATCAY
MT000150 1386 activating transcription factor 2 ATF2
MT000697 9140 autophagy related 12 ATG12
MT000869 23130 autophagy related 2A ATG2A
MT001133 55102 autophagy related 2B ATG2B
MT001259 64422 autophagy related 3 ATG3
MT001490 115201 autophagy related 4A, cysteine peptidase ATG4A
MT000872 23192 autophagy related 4B, cysteine peptidase ATG4B
MT001435 84938 autophagy related 4C, cysteine peptidase ATG4C
MT001438 84971 autophagy related 4D, cysteine peptidase ATG4D
MT000711 9474 autophagy related 5 ATG5
MT000788 10533 autophagy related 7 ATG7
MT001303 79065 autophagy related 9A ATG9A
MT000047 471 5-aminoimidazole-4-carboxamide ribonucleotide
formyltransferase/IMP cyclohydrolase		 ATIC
MT000048 487 ATPase, Ca++ transporting, cardiac muscle, fast twitch 1 ATP2A1
MT000049 498 ATP synthase, H+ transporting, mitochondrial F1 complex, α
subunit 1, cardiac muscle		 ATP5A1
MT000051 506 ATP synthase, H+ transporting, mitochondrial F1 complex, β
polypeptide		 ATP5B
MT000052 509 ATP synthase, H+ transporting, mitochondrial F1 complex, γ
polypeptide 1		 ATP5C1
MT000053 513 ATP synthase, H+ transporting, mitochondrial F1 complex, δ
subunit		 ATP5D
MT000054 514 ATP synthase, H+ transporting, mitochondrial F1 complex, ε
subunit		 ATP5E
MT001670 432369 ATP synthase, H+ transporting, mitochondrial F1 complex, ε
subunit pseudogene 2		 ATP5EP2
MT000055 515 ATP synthase, H+ transporting, mitochondrial Fo complex,
subunit B1		 ATP5F1
MT000056 516 ATP synthase, H+ transporting, mitochondrial Fo complex,
subunit C1 (subunit 9)		 ATP5G1
MT000057 517 ATP synthase, H+ transporting, mitochondrial Fo complex,
subunit C2 (subunit 9)		 ATP5G2
MT000058 518 ATP synthase, H+ transporting, mitochondrial Fo complex,
subunit C3 (subunit 9)		 ATP5G3
MT000783 10476 ATP synthase, H+ transporting, mitochondrial Fo complex,
subunit d		 ATP5H
MT000059 521 ATP synthase, H+ transporting, mitochondrial Fo complex,
subunit E		 ATP5I
MT000060 522 ATP synthase, H+ transporting, mitochondrial Fo complex,
subunit F6		 ATP5J
MT000720 9551 ATP synthase, H+ transporting, mitochondrial Fo complex,
subunit F2		 ATP5J2
MT000798 10632 ATP synthase, H+ transporting, mitochondrial Fo complex,
subunit G		 ATP5L
MT001614 267020 ATP synthase, H+ transporting, mitochondrial Fo complex,
subunit G2		 ATP5L2
MT000064 539 ATP synthase, H+ transporting, mitochondrial F1 complex, O
subunit		 ATP5O
MT000959 27109 ATP synthase, H+ transporting, mitochondrial Fo complex,
subunit s (factor B)		 ATP5S
MT001132 55101 ATP5S-like ATP5SL
MT000368 4508 ['ATP synthase F0 subunit 6'] ATP6
MT000061 523 ATPase, H+ transporting, lysosomal 70kDa, V1 subunit A ATP6V1A
MT000062 529 ATPase, H+ transporting, lysosomal 31kDa, V1 subunit E1 ATP6V1E1
MT000063 538 ATPase, Cu++ transporting, α polypeptide ATP7A
MT000065 540 ATPase, Cu++ transporting, β polypeptide ATP7B
MT000369 4509 ['ATP synthase F0 subunit 8'] ATP8
MT001265 64756 ATP synthase mitochondrial F1 complex assembly factor 1 ATPAF1
MT001462 91647 ATP synthase mitochondrial F1 complex assembly factor 2 ATPAF2
MT001476 93974 ATPase inhibitory factor 1 ATPIF1
MT000359 4287 ataxin 3 ATXN3
MT000066 549 AU RNA binding protein/enoyl-CoA hydratase AUH
MT001117 54998 aurora kinase A interacting protein 1 AURKAIP1
MT000067 551 arginine vasopressin AVP
MT001484 113451 antizyme inhibitor 2 AZIN2
MT000068 572 BCL2-associated agonist of cell death BAD
MT000069 573 BCL2-associated athanogene BAG1
MT000718 9529 BCL2-associated athanogene 5 BAG5
MT000070 578 BCL2-antagonist/killer 1 BAK1
MT000071 581 BCL2-associated X protein BAX
MT000960 27113 BCL2 binding component 3 BBC3
MT000656 8424 butyroβine (γ), 2-oxoglutarate dioxygenase (γ-butyroβine
hydroxylase) 1		 BBOX1
MT000754 10134 B-cell receptor-associated protein 31 BCAP31
MT000072 586 branched chain amino-acid transaminase 1, cytosolic BCAT1
MT000073 587 branched chain amino-acid transaminase 2, mitochondrial BCAT2
MT000074 593 branched chain keto acid dehydrogenase E1, α polypeptide BCKDHA
MT000075 594 branched chain keto acid dehydrogenase E1, β polypeptide BCKDHB
MT000767 10295 branched chain ketoacid dehydrogenase kinase BCKDK
MT000076 596 B-cell CLL/lymphoma 2 BCL2
MT000077 597 BCL2-related protein A1 BCL2A1
MT000078 598 BCL2-like 1 BCL2L1
MT000743 10017 BCL2-like 10 (apoptosis facilitator) BCL2L10
MT000744 10018 BCL2-like 11 (apoptosis facilitator) BCL2L11
MT000908 23786 BCL2-like 13 (apoptosis facilitator) BCL2L13
MT000079 599 BCL2-like 2 BCL2L2
MT001385 83875 β-carotene oxygenase 2 BCO2
MT000080 617 BC1 (ubiquinol-cytochrome c reductase) synthesis-like BCS1L
MT000081 622 3-hydroxybutyrate dehydrogenase, type 1 BDH1
MT001195 56898 3-hydroxybutyrate dehydrogenase, type 2 BDH2
MT000082 627 brain-derived neurotrophic factor BDNF
MT000670 8678 beclin 1, autophagy related BECN1
MT000083 631 beaded filament structural protein 1, filensin BFSP1
MT001578 168620 basic helix-loop-helix family, member a15 BHLHA15
MT000084 637 BH3 interacting domain death agonist BID
MT000085 638 BCL2-interacting killer (apoptosis-inducing) BIK
MT001669 414899 BH3-like motif containing, cell death inducer BLID
MT000243 2647 biogenesis of lysosomal organelles complex-1, subunit 1 BLOC1S1
MT001616 282991 biogenesis of lysosomal organelles complex-1, subunit 2 BLOC1S2
MT001451 90427 Bcl2 modifying factor BMF
MT000086 662 BCL2/adenovirus E1B 19kDa interacting protein 1 BNIP1
MT000087 664 BCL2/adenovirus E1B 19kDa interacting protein 3 BNIP3
MT000088 665 BCL2/adenovirus E1B 19kDa interacting protein 3-like BNIP3L
MT000089 666 BCL2-related ovarian killer BOK
MT001018 51027 bolA family member 1 BOLA1
MT001698 100294715 Polymicrogyria, bilateral occipital BOP
MT000090 670 biphenyl hydrolase-like (serine hydrolase) BPHL
MT000091 673 B-Raf proto-oncogene, serine/threonine kinase BRAF
MT000816 10902 bromodomain containing 8 BRD8
MT001551 140707 BRI3 binding protein BRI3BP
MT001636 339479 bone morphogenetic protein/retinoic acid inducible neural-
specific 3		 BRINP3
MT000092 682 basigin (Ok blood group) BSG
MT000093 686 biotinidase BTD
MT000703 9256 benzodiazepine receptor (peripheral) associated protein 1 BZRAP1
MT000836 11067 chromosome 10 open reading frame 10 C10orf10
MT001235 60314 chromosome 12 open reading frame 10 C12orf10
MT001461 91574 chromosome 12 open reading frame 65 C12orf65
MT001123 55017 chromosome 14 open reading frame 119 C14orf119
MT001338 80017 chromosome 14 open reading frame 159 C14orf159
MT000722 9556 chromosome 14 open reading frame 2 C14orf2
MT001682 643338 chromosome 15 open reading frame 62 C15orf62
MT001625 284184 chromosome 17 open reading frame 89 C17orf89
MT001377 83636 chromosome 19 open reading frame 12 C19orf12
MT001520 125988 chromosome 19 open reading frame 70 C19orf70
MT000095 708 complement component 1, q subcomponent binding protein C1QBP
MT000650 8209 chromosome 21 open reading frame 33 C21orf33
MT001309 79568 chromosome 2 open reading frame 47 C2orf47
MT001665 401207 chromosome 5 open reading frame 63 C5orf63
MT001601 221545 chromosome 6 open reading frame 136 C6orf136
MT001042 51250 chromosome 6 open reading frame 203 C6orf203
MT001567 154791 chromosome 7 open reading frame 55 C7orf55
MT001399 84270 chromosome 9 open reading frame 89 C9orf89
MT000097 763 carbonic anhydrase VA, mitochondrial CA5A
MT000849 11238 carbonic anhydrase VB, mitochondrial CA5B
MT001639 340591 carbonic anhydrase VB pseudogene 1 CA5BP1
MT001442 85438 calcium-binding protein, spermatid-specific 1 CABS1
MT000099 815 calcium/calmodulin-dependent protein kinase II α CAMK2A
MT000100 821 calnexin CANX
MT000840 11132 calpain 10 CAPN10
MT001294 65981 caprin family member 2 CAPRIN2
MT001173 55739 carbohydrate kinase domain containing CARKD
MT001311 79587 cysteinyl-tRNA synthetase 2, mitochondrial (putative) CARS2
MT000101 834 caspase 1, apoptosis-related cysteine peptidase CASP1
MT000102 835 caspase 2, apoptosis-related cysteine peptidase CASP2
MT000103 836 caspase 3, apoptosis-related cysteine peptidase CASP3
MT000104 837 caspase 4, apoptosis-related cysteine peptidase CASP4
MT000105 840 caspase 7, apoptosis-related cysteine peptidase CASP7
MT000106 841 caspase 8, apoptosis-related cysteine peptidase CASP8
MT000739 9994 caspase 8 associated protein 2 CASP8AP2
MT000107 842 caspase 9, apoptosis-related cysteine peptidase CASP9
MT000108 844 calsequestrin 1 (fast-twitch, skeletal muscle) CASQ1
MT000109 847 catalase CAT
MT000110 858 caveolin 2 CAV2
MT001428 84869 carbonyl reductase 4 CBR4
MT001230 57805 cell cycle and apoptosis regulator 2 CCAR2
MT001189 56267 cysteine conjugate-β lyase 2 CCBL2
MT001121 55013 coiled-coil domain containing 109B CCDC109B
MT001264 64753 coiled-coil domain containing 136 CCDC136
MT001320 79714 coiled-coil domain containing 51 CCDC51
MT001531 131076 coiled-coil domain containing 58 CCDC58
MT001239 60492 coiled-coil domain containing 90B CCDC90B
MT000112 885 cholecystokinin CCK
MT000795 10574 chaperonin containing TCP1, subunit 7 (eta) CCT7
MT001693 100133941 CD24 molecule CD24
MT000810 10849 CD3e molecule, ε associated protein CD3EAP
MT000113 983 cyclin-dependent kinase 1 CDK1
MT000114 1022 cyclin-dependent kinase 7 CDK7
MT000115 1029 cyclin-dependent kinase inhibitor 2A CDKN2A
MT000676 8760 CDP-diacylglycerol synthase (phosphatidate
cytidylyltransferase) 2		 CDS2
MT000116 1050 CCAAT/enhancer binding protein (C/EBP), α CEBPA
MT000974 27440 cat eye syndrome chromosome region, candidate 5 CECR5
MT001433 84902 centrosomal protein 89kDa CEP89
MT001267 64781 ceramide kinase CERK
MT000911 25790 cilia and flagella associated protein 45 CFAP45
MT000117 1103 choline O-acetyltransferase CHAT
MT001503 118487 coiled-coil-helix-coiled-coil-helix domain containing 1 CHCHD1
MT001663 400916 coiled-coil-helix-coiled-coil-helix domain containing 10 CHCHD10
MT001036 51142 coiled-coil-helix-coiled-coil-helix domain containing 2 CHCHD2
MT001684 645345 coiled-coil-helix-coiled-coil-helix domain containing 2
pseudogene 9		 CHCHD2P9
MT001101 54927 coiled-coil-helix-coiled-coil-helix domain containing 3 CHCHD3
MT001533 131474 coiled-coil-helix-coiled-coil-helix domain containing 4 CHCHD4
MT001398 84269 coiled-coil-helix-coiled-coil-helix domain containing 5 CHCHD5
MT001405 84303 coiled-coil-helix-coiled-coil-helix domain containing 6 CHCHD6
MT001308 79145 coiled-coil-helix-coiled-coil-helix domain containing 7 CHCHD7
MT001158 55349 choline dehydrogenase CHDH
MT000928 25978 charged multivesicular body protein 2B CHMP2B
MT001310 79586 chondroitin polymerizing factor CHPF
MT001207 57019 cytokine induced apoptosis inhibitor 1 CIAPIN1
MT000118 1149 cell death-inducing DFFA-like effector a CIDEA
MT001181 55847 CDGSH iron sulfur domain 1 CISD1
MT001678 493856 CDGSH iron sulfur domain 2 CISD2
MT001622 284106 CDGSH iron sulfur domain 3 CISD3
MT000119 1152 creatine kinase, brain CKB
MT001679 548596 creatine kinase, mitochondrial 1A CKMT1A
MT000120 1160 creatine kinase, mitochondrial 2 (sarcomeric) CKMT2
MT000123 1192 chloride intracellular channel 1 CLIC1
MT000922 25932 chloride intracellular channel 4 CLIC4
MT000125 1201 ceroid-lipofuscinosis, neuronal 3 CLN3
MT000208 2055 ceroid-lipofuscinosis, neuronal 8 (epilepsy, progressive
with mental retardation)		 CLN8
MT001362 81570 ClpB caseinolytic peptidase B homolog (E. coli) CLPB
MT000649 8192 caseinolytic mitochondrial matrix peptidase proteolytic
subunit		 CLPP
MT000809 10845 caseinolytic mitochondrial matrix peptidase chaperone
subunit		 CLPX
MT000126 1213 clathrin, heavy chain (Hc) CLTC
MT000122 1191 clusterin CLU
MT000876 23277 clustered mitochondria (cluA/CLU1) homolog CLUH
MT001580 171425 citrate lyase β like CLYBL
MT001563 152100 C-x(9)-C motif containing 1 CMC1
MT001198 56942 C-x(9)-C motif containing 2 CMC2
MT001696 100272147 C-x(9)-C motif containing 4 CMC4
MT001528 129607 cytidine monophosphate (UMP-CMP) kinase 2, mitochondrial CMPK2
MT000127 1267 2',3'-cyclic nucleotide 3' phosphodiesterase CNP
MT001174 55744 cytochrome c oxidase assembly factor 1 homolog (S.
cerevisiae)		 COA1
MT000976 28958 cytochrome c oxidase assembly factor 3 COA3
MT001049 51287 cytochrome c oxidase assembly factor 4 homolog (S.
cerevisiae)		 COA4
MT001677 493753 cytochrome c oxidase assembly factor 5 COA5
MT001656 388753 cytochrome c oxidase assembly factor 6 COA6
MT001293 65260 cytochrome c oxidase assembly factor 7 (putative) COA7
MT001357 80347 CoA synthase COASY
MT000749 10087 collagen, type IV, α 3 (Goodpasture antigen) binding
protein		 COL4A3BP
MT000128 1312 catechol-O-methyltransferase COMT
MT001505 118881 catechol-O-methyltransferase domain containing 1 COMTD1
MT001474 93058 coenzyme Q10 homolog A (S. cerevisiae) COQ10A
MT001346 80219 coenzyme Q10 homolog B (S. cerevisiae) COQ10B
MT000966 27235 coenzyme Q2 4-hydroxybenzoate polyprenyltransferase COQ2
MT001075 51805 coenzyme Q3 methyltransferase COQ3
MT001035 51117 coenzyme Q4 COQ4
MT001401 84274 coenzyme Q5 homolog, methyltransferase (S. cerevisiae) COQ5
MT001009 51004 coenzyme Q6 monooxygenase COQ6
MT000760 10229 coenzyme Q7 homolog, ubiquinone (yeast) COQ7
MT001206 57017 coenzyme Q9 COQ9
MT000370 4512 ['cytochrome c oxidase subunit I'] COX1
MT000141 1352 COX10 heme A:farnesyltransferase cytochrome c oxidase
assembly factor		 COX10
MT000142 1353 COX11 cytochrome c oxidase copper chaperone COX11
MT001439 84987 COX14 cytochrome c oxidase assembly factor COX14
MT000143 1355 cytochrome c oxidase assembly homolog 15 (yeast) COX15
MT001041 51241 COX16 cytochrome c oxidase assembly homolog (S. cerevisiae) COX16
MT000748 10063 COX17 cytochrome c oxidase copper chaperone COX17
MT001632 285521 COX18 cytochrome c oxidase assembly factor COX18
MT000371 4513 ['cytochrome c oxidase subunit II'] COX2
MT001496 116228 COX20 cytochrome c oxidase assembly factor COX20
MT000372 4514 cytochrome c oxidase III COX3
MT000129 1327 cytochrome c oxidase subunit IV isoform 1 COX4I1
MT001419 84701 cytochrome c oxidase subunit IV isoform 2 (lung) COX4I2
MT000705 9377 cytochrome c oxidase subunit Va COX5A
MT000130 1329 cytochrome c oxidase subunit Vb COX5B
MT000131 1337 cytochrome c oxidase subunit VIa polypeptide 1 COX6A1
MT000132 1339 cytochrome c oxidase subunit VIa polypeptide 2 COX6A2
MT000133 1340 cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) COX6B1
MT001519 125965 cytochrome c oxidase subunit VIb polypeptide 2 (testis) COX6B2
MT000134 1345 cytochrome c oxidase subunit VIc COX6C
MT000135 1346 cytochrome c oxidase subunit VIIa polypeptide 1 (muscle) COX7A1
MT000136 1347 cytochrome c oxidase subunit VIIa polypeptide 2 (liver) COX7A2
MT000699 9167 cytochrome c oxidase subunit VIIa polypeptide 2 like COX7A2L
MT000137 1348 cytochrome c oxidase subunit VIIa polypeptide 2 (liver)
pseudogene 2		 COX7A2P2
MT000138 1349 cytochrome c oxidase subunit VIIb COX7B
MT001579 170712 cytochrome c oxidase subunit VIIb2 COX7B2
MT000139 1350 cytochrome c oxidase subunit VIIc COX7C
MT000140 1351 cytochrome c oxidase subunit VIIIA (ubiquitous) COX8A
MT001641 341947 cytochrome c oxidase subunit VIIIC COX8C
MT000144 1371 coproporphyrinogen oxidase CPOX
MT000145 1373 carbamoyl-phosphate synthase 1, mitochondrial CPS1
MT000146 1374 carnitine palmitoyltransferase 1A (liver) CPT1A
MT000147 1375 carnitine palmitoyltransferase 1B (muscle) CPT1B
MT001521 126129 carnitine palmitoyltransferase 1C CPT1C
MT000148 1376 carnitine palmitoyltransferase 2 CPT2
MT000149 1384 carnitine O-acetyltransferase CRAT
MT001093 54675 cardiolipin synthase 1 CRLS1
MT001094 54677 carnitine O-octanoyltransferase CROT
MT000151 1407 cryptochrome circadian clock 1 CRY1
MT000152 1410 crystallin, α B CRYAB
MT000153 1428 crystallin, mu CRYM
MT000154 1431 citrate synthase CS
MT000638 7812 cold shock domain containing E1, RNA-binding CSDE1
MT001191 56474 CTP synthase 2 CTPS2
MT000488 5476 cathepsin A CTSA
MT000157 1508 cathepsin B CTSB
MT001449 90353 cytosolic thiouridylase subunit 1 CTU1
MT001645 348180 cytosolic thiouridylase subunit 2 homolog (S. pombe) CTU2
MT000158 1525 coxsackie virus and adenovirus receptor CXADR
MT001612 256643 chromosome X open reading frame 23 CXorf23
MT000159 1528 cytochrome b5 type A (microsomal) CYB5A
MT001360 80777 cytochrome b5 type B (outer mitochondrial membrane) CYB5B
MT001071 51706 cytochrome b5 reductase 1 CYB5R1
MT001069 51700 cytochrome b5 reductase 2 CYB5R2
MT000183 1727 cytochrome b5 reductase 3 CYB5R3
MT000160 1535 cytochrome b-245, α polypeptide CYBA
MT000161 1536 cytochrome b-245, β polypeptide CYBB
MT000162 1537 cytochrome c-1 CYC1
MT001081 54205 cytochrome c, somatic CYCS
MT000167 1583 cytochrome P450, family 11, subfamily A, polypeptide 1 CYP11A1
MT000168 1584 cytochrome P450, family 11, subfamily B, polypeptide 1 CYP11B1
MT000169 1585 cytochrome P450, family 11, subfamily B, polypeptide 2 CYP11B2
MT000170 1586 cytochrome P450, family 17, subfamily A, polypeptide 1 CYP17A1
MT000163 1543 cytochrome P450, family 1, subfamily A, polypeptide 1 CYP1A1
MT000164 1545 cytochrome P450, family 1, subfamily B, polypeptide 1 CYP1B1
MT000171 1591 cytochrome P450, family 24, subfamily A, polypeptide 1 CYP24A1
MT000172 1593 cytochrome P450, family 27, subfamily A, polypeptide 1 CYP27A1
MT000173 1594 cytochrome P450, family 27, subfamily B, polypeptide 1 CYP27B1
MT000165 1565 cytochrome P450, family 2, subfamily D, polypeptide 6 CYP2D6
MT000166 1571 cytochrome P450, family 2, subfamily E, polypeptide 1 CYP2E1
MT000374 4519 ['cytochrome b'] CYTB
MT001686 728294 D-2-hydroxyglutarate dehydrogenase D2HGDH
MT001577 168002 dishevelled-binding antagonist of β-catenin 2 DACT2
MT000174 1610 D-amino-acid oxidase DAO
MT001613 267012 D-amino acid oxidase activator DAOA
MT000639 7818 death associated protein 3 DAP3
MT001138 55157 aspartyl-tRNA synthetase 2, mitochondrial DARS2
MT000175 1622 diazepam binding inhibitor (GABA receptor modulator, acyl-
CoA binding protein)		 DBI
MT000176 1629 dihydrolipoamide branched chain transacylase E2 DBT
MT000683 8816 DDB1 and CUL4 associated factor 5 DCAF5
MT001331 79877 dephospho-CoA kinase domain containing DCAKD
MT000977 28960 decapping enzyme, scavenger DCPS
MT000897 23576 dimethylarginine dimethylaminohydrolase 1 DDAH1
MT000895 23564 dimethylarginine dimethylaminohydrolase 2 DDAH2
MT001089 54541 DNA-damage-inducible transcript 4 DDIT4
MT000706 9416 DEAD (Asp-Glu-Ala-Asp) box polypeptide 23 DDX23
MT001178 55794 DEAD (Asp-Glu-Ala-Asp) box polypeptide 28 DDX28
MT000178 1654 DEAD (Asp-Glu-Ala-Asp) box helicase 3, X-linked DDX3X
MT000179 1666 2,4-dienoyl CoA reductase 1, mitochondrial DECR1
MT000663 8560 δ(4)-desaturase, sphingolipid 1 DEGS1
MT001416 84649 diacylglycerol O-acyltransferase 2 DGAT2
MT000181 1716 deoxyguanosine kinase DGUOK
MT001587 200895 dihydrofolate reductase-like 1 DHFRL1
MT000182 1723 dihydroorotate dehydrogenase (quinone) DHODH
MT001494 115817 dehydrogenase/reductase (SDR family) member 1 DHRS1
MT000759 10202 dehydrogenase/reductase (SDR family) member 2 DHRS2
MT000815 10901 dehydrogenase/reductase (SDR family) member 4 DHRS4
MT001163 55526 dehydrogenase E1 and transketolase domain containing 1 DHTKD1
MT001085 54505 DEAH (Asp-Glu-Ala-His) box polypeptide 29 DHX29
MT000861 22907 DEAH (Asp-Glu-Ala-His) box helicase 30 DHX30
MT001177 55760 DEAH (Asp-Glu-Ala-His) box polypeptide 32 DHX32
MT001457 90957 DEAH (Asp-Glu-Ala-Asp/His) box polypeptide 57 DHX57
MT001192 56616 diablo, IAP-binding mitochondrial protein DIABLO
MT000184 1730 diaphanous-related formin 2 DIAPH2
MT000965 27185 disrupted in schizophrenia 1 DISC1
MT000185 1737 dihydrolipoamide S-acetyltransferase DLAT
MT000186 1738 dihydrolipoamide dehydrogenase DLD
MT000187 1743 dihydrolipoamide S-succinyltransferase (E2 component of 2-
oxo-glutarate complex)		 DLST
MT000998 29958 dimethylglycine dehydrogenase DMGDH
MT000189 1760 dystrophia myotonica-protein kinase DMPK
MT000190 1763 DNA replication helicase/nuclease 2 DNA2
MT000297 3301 DnaJ (Hsp40) homolog, subfamily A, member 1 DNAJA1
MT000695 9093 DnaJ (Hsp40) homolog, subfamily A, member 3 DNAJA3
MT001172 55735 DnaJ (Hsp40) homolog, subfamily C, member 11 DNAJC11
MT000990 29103 DnaJ (Hsp40) homolog, subfamily C, member 15 DNAJC15
MT001532 131118 DnaJ (Hsp40) homolog, subfamily C, member 19 DNAJC19
MT001048 51277 DnaJ (Hsp40) homolog, subfamily C, member 27 DNAJC27
MT001403 84277 DnaJ (Hsp40) homolog, subfamily C, member 30 DNAJC30
MT000308 3338 DnaJ (Hsp40) homolog, subfamily C, member 4 DNAJC4
MT001356 80331 DnaJ (Hsp40) homolog, subfamily C, member 5 DNAJC5
MT001687 728489 DNL-type zinc finger DNLZ
MT000746 10059 dynamin 1-like DNM1L
MT000933 26052 dynamin 3 DNM3
MT000191 1808 dihydropyrimidinase-like 2 DPYSL2
MT000192 1819 developmentally regulated GTP binding protein 2 DRG2
MT000193 1832 desmoplakin DSP
MT000194 1841 deoxythymidylate kinase (thymidylate kinase) DTYMK
MT001100 54920 dihydrouridine synthase 2 DUS2
MT001245 63904 dual specificity phosphatase 21 DUSP21
MT001299 78986 dual specificity phosphatase 26 (putative) DUSP26
MT000195 1854 deoxyuridine triphosphatase DUT
MT000667 8655 dynein, light chain, LC8-type 1 DYNLL1
MT001552 140735 dynein, light chain, LC8-type 2 DYNLL2
MT000196 1869 E2F transcription factor 1 E2F1
MT001514 124454 glutamyl-tRNA synthetase 2, mitochondrial EARS2
MT000198 1891 enoyl CoA hydratase 1, peroxisomal ECH1
MT001149 55268 enoyl CoA hydratase domain containing 2 ECHDC2
MT001323 79746 enoyl CoA hydratase domain containing 3 ECHDC3