MitoProteome Database

MT000361

Gene Information

Entrez Gene ID4329
Gene Namealdehyde dehydrogenase 6 family, member A1
Gene SymbolALDH6A1
SpeciesHomo sapiens
Gene Ontology (GO Annotations)
GO IDSourceTypeDescription
GO:0070062 IDA:UniProtCextracellular vesicular exosome
GO:0005759 TAS:ReactomeCmitochondrial matrix
GO:0005739 NAS:UniProtKBCmitochondrion
GO:0005634 IDA:HPACnucleus
GO:0000062 ISS:UniProtKBFfatty-acyl-CoA binding
GO:0018478 ISS:UniProtKBFmalonate-semialdehyde dehydrogenase (acetylating) activity
GO:0004491 ISS:UniProtKBFmethylmalonate-semialdehyde dehydrogenase (acylating) activity
GO:0044822 IDA:UniProtKBFpoly(A) RNA binding
GO:0009083 TAS:ReactomePbranched-chain amino acid catabolic process
GO:0050873 IEA:EnsemblPbrown fat cell differentiation
GO:0034641 TAS:ReactomePcellular nitrogen compound metabolic process
GO:0044281 TAS:ReactomePsmall molecule metabolic process
GO:0006210 IMP:BHF-UCLPthymine catabolic process
GO:0019859 ISS:UniProtKBPthymine metabolic process
GO:0006574 IMP:BHF-UCLPvaline catabolic process
GO:0006573 ISS:UniProtKBPvaline metabolic process
KEGG Pathway Links
KEGG Pathway IDDescription
hsa00410beta-Alanine metabolism
ko00410beta-Alanine metabolism
hsa01200Carbon metabolism
ko01200Carbon metabolism
hsa00562Inositol phosphate metabolism
ko00562Inositol phosphate metabolism
hsa_M00013Malonate semialdehyde pathway, propanoyl-CoA => Acetyl-CoA
M00013Malonate semialdehyde pathway, propanoyl-CoA => Acetyl-CoA
hsa01100Metabolic pathways
hsa00640Propanoate metabolism
ko00640Propanoate metabolism
hsa00280Valine, leucine and isoleucine degradation
ko00280Valine, leucine and isoleucine degradation
BIOCYC Pathway Links
BIOCYC Pathway IDDescription
BETA-ALA-DEGRADATION-I-PWYbeta-alanine degradation I
VALDEG-PWYvaline degradation I
REACTOME Pathway Links
REACTOME Pathway IDDescription
REACT_197Branched-chain amino acid catabolism
REACT_111217Metabolism
REACT_13Metabolism of amino acids and derivatives