MitoProteome Database

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MT000656

Gene Information

Entrez Gene ID8424
Gene Namebutyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetaine hydroxylase) 1
Gene SymbolBBOX1
SpeciesHomo sapiens
Gene Ontology (GO Annotations)
GO IDSourceTypeDescription
GO:0005829 TAS:ReactomeCcytosol
GO:0070062 IDA:UniProtCextracellular vesicular exosome
GO:0005739 IEA:EnsemblCmitochondrion
GO:0008336 IDA:UniProtKBFgamma-butyrobetaine dioxygenase activity
GO:0005506 IEA:InterProFiron ion binding
GO:0008270 IDA:UniProtKBFzinc ion binding
GO:0045329 IDA:UniProtKBPcarnitine biosynthetic process
GO:0034641 TAS:ReactomePcellular nitrogen compound metabolic process
GO:0044281 TAS:ReactomePsmall molecule metabolic process
KEGG Pathway Links
KEGG Pathway IDDescription
hsa00310Lysine degradation
ko00310Lysine degradation
BIOCYC Pathway Links
BIOCYC Pathway IDDescription
PWY-6100L-carnitine biosynthesis
PWY-6100L-carnitine biosynthesis
REACTOME Pathway Links
REACTOME Pathway IDDescription
REACT_2125Carnitine synthesis
REACT_111217Metabolism
REACT_13Metabolism of amino acids and derivatives