MitoProteome Database

MT001094

UniProt Annotations

Entry Information
Gene Namecarnitine O-octanoyltransferase
Protein EntryOCTC_HUMAN
UniProt IDQ9UKG9
SpeciesHuman
Comments
Comment typeDescription
Alternative Products Event=Alternative splicing; Named isoforms=3; Name=1; IsoId=Q9UKG9-1; Sequence=Displayed; Name=2; IsoId=Q9UKG9-2; Sequence=VSP_045213, VSP_045214; Name=3; IsoId=Q9UKG9-3; Sequence=VSP_046953; Note=No experimental confirmation available. Gene prediction based on cDNA data.;
Catalytic Activity Octanoyl-CoA + L-carnitine = CoA + L- octanoylcarnitine.
Function Beta-oxidation of fatty acids. The highest activity concerns the C6 to C10 chain length substrate. Converts the end product of pristanic acid beta oxidation, 4,8-dimethylnonanoyl- CoA, to its corresponding carnitine ester. {ECO:0000269|PubMed:10486279}.
Pathway Lipid metabolism; fatty acid beta-oxidation.
Similarity Belongs to the carnitine/choline acetyltransferase family. {ECO:0000305}.
Subcellular Location Peroxisome {ECO:0000305}.
Subunit Monomer. {ECO:0000305|PubMed:10486279}.