Home
MitoProteome Human Mitochondrial Protein Database
MitoProteome Database
New search
|
Record Overview
|
Ontology/Pathway Information
|
Domain Information
|
UniProt Annotations
|
Related Proteins
MT001094
UniProt Annotations
Entry Information
Gene Name
carnitine O-octanoyltransferase
Protein Entry
OCTC_HUMAN
UniProt ID
Q9UKG9
Species
Human
Comments
Comment type
Description
Alternative Products
Event=Alternative splicing; Named isoforms=3; Name=1; IsoId=Q9UKG9-1; Sequence=Displayed; Name=2; IsoId=Q9UKG9-2; Sequence=VSP_045213, VSP_045214; Name=3; IsoId=Q9UKG9-3; Sequence=VSP_046953; Note=No experimental confirmation available. Gene prediction based on cDNA data.;
Catalytic Activity
Octanoyl-CoA + L-carnitine = CoA + L- octanoylcarnitine.
Function
Beta-oxidation of fatty acids. The highest activity concerns the C6 to C10 chain length substrate. Converts the end product of pristanic acid beta oxidation, 4,8-dimethylnonanoyl- CoA, to its corresponding carnitine ester. {ECO:0000269|PubMed:10486279}.
Pathway
Lipid metabolism; fatty acid beta-oxidation.
Similarity
Belongs to the carnitine/choline acetyltransferase family. {ECO:0000305}.
Subcellular Location
Peroxisome {ECO:0000305}.
Subunit
Monomer. {ECO:0000305|PubMed:10486279}.
MitoProteome Human Mitochondrial Protein Database
Contact us